| Catalog_no | AB0812 |
| Product_name | BCKDHB Antibody (N-term) |
| Category | 抗原抗体 |
| Applications | WB, IHC-P |
| Reactivity | H |
| Size | 100μL/50μL |
| Price | 2000.00/1100.00 |
| immunogen | HUMAN:41-70 |
| Specificity | This BCKDHB antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB. |
| Dilution | ,1:500;,1:500;IF,1:25;WB,1:1000;FC,1:10~50; |
| Purification | Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is purified through a protein A column, followed by peptide affinity purification. |
| othername | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, Branched-chain alpha-keto acid dehydrogenase E1 component beta chain, BCKDE1B, BCKDH E1-beta, BCKDHB |
| Isotype | Rabbit Ig |
| Background | Branched-chain keto acid dehydrogenase is a multienzyme
complex associated with the inner membrane of mitochondria, and
functions in the catabolism of branched-chain amino acids. The
complex consists of multiple copies of 3 components: branched-chain
alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2)
and lipoamide dehydrogenase (E3). This gene encodes the E1 beta
subunit, and mutations therein have been associated with maple
syrup urine disease (MSUD), type 1B, a disease characterized by a
maple syrup odor to the urine in addition to mental and physical
retardation, and feeding problems. |
| Instructions | 
查看与下载 |
| Share |
|
