| Catalog_no | AB1031 |
| Product_name | PCCA Antibody (Center) |
| Category | 抗原抗体 |
| Applications | WB |
| Reactivity | H, Rat |
| Size | 100μL/50μL |
| Price | 2000.00/1100.00 |
| immunogen | HUMAN:362-390 |
| Specificity | This PCCA antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 362-390 amino acids from the Central region of human PCCA. |
| Dilution | IHC-P,1:25;IHC-P,1:25;IHC-P,1:25;IHC-P,1:25;WB,1:2000; |
| Purification | Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is purified through a protein A column, followed by peptide affinity purification. |
| othername | Propionyl-CoA carboxylase alpha chain, mitochondrial, PCCase subunit alpha, Propanoyl-CoA:carbon dioxide ligase subunit alpha, PCCA |
| Isotype | Rabbit Ig |
| Background | The protein encoded by this gene is the alpha subunit of
the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase.
PCCA encodes the biotin-binding region of this enzyme. Mutations in
either PCCA or PCCB (encoding the beta subunit) lead to an enzyme
deficiency resulting in propionic acidemia. Multiple transcript
variants encoding different isoforms have been found for this gene. |
| Instructions | 
查看与下载 |
| Share |
|
