L2HGDH Antibody (Center)

日期:2020-08-01 00:36 人气:
Catalog_no AB0755
Product_name L2HGDH Antibody (Center)
Category 抗原抗体
Applications WB, IHC-P, FC
Reactivity H, M
Size 100μL/50μL
Price 2000.00/1100.00
immunogen HUMAN:132-159
Specificity This L2HGDH antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 132-159 amino acids from the Central region of human L2HGDH.
Dilution WB,1:1000;
Purification Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is purified through a protein A column, followed by peptide affinity purification.
othername L-2-hydroxyglutarate dehydrogenase, mitochondrial, Duranin, L2HGDH, C14orf160
Isotype Rabbit Ig
Background This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.
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