PCCA Antibody (Center)

日期：2020-08-01 00:36　人气：

Catalog_no	AB1031
Product_name	PCCA Antibody (Center)
Category	抗原抗体
Applications	WB
Reactivity	H, Rat
Size	100μL/50μL
Price	2000.00/1100.00
immunogen	HUMAN:362-390
Specificity	This PCCA antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 362-390 amino acids from the Central region of human PCCA.
Dilution	IHC-P,1:25;IHC-P,1:25;IHC-P,1:25;IHC-P,1:25;WB,1:2000;
Purification	Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide. This antibody is purified through a protein A column, followed by peptide affinity purification.
othername	Propionyl-CoA carboxylase alpha chain, mitochondrial, PCCase subunit alpha, Propanoyl-CoA:carbon dioxide ligase subunit alpha, PCCA
Isotype	Rabbit Ig
Background	The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.
Instructions	查看与下载